The frequency of Turner syndrome (TS) is approximately 1 in 2000 live-born female infants. Turner syndrome is caused by the absence of one set of genes from the short arm of one X chromosome and has an unfavorable affect on the endocrine and cardiovascular systems. A 45-year old housewife who no history of systemic disease presented to our emergency department with complaints of chest pain which had begun three days prior to admission. After initial examination and management, the echocardiogram and computed tomogram showed the presence of type B Stanford aortic dissection. All doctors should remain alert to the possibility of aortic dissection in patients with TS who suffer chest pain, since early detection of aortic dissection may save the lives of patients with TS.
Keywords: Turner syndrome, aortic dissection